• Users Online: 113
  • Home
  • Print this page
  • Email this page
Home About us Editorial board Search Ahead of print Current issue Archives Submit article Instructions Subscribe Contacts Login 
Year : 2017  |  Volume : 12  |  Issue : 2  |  Page : 74-80

An overview of abnormal pulmonary venous connection in children

1 Department of Paediatrics, Bayero University/Aminu Kano Teaching Hospital, Kano, Nigeria
2 Department of Paediatrics, Usman Dan Fodio University/Usman Dan Fodio University Teaching Hospital, Sokoto, Nigeria

Correspondence Address:
Mustafa O Asani
Department of Paediatrics, Bayero University/Aminu Kano Teaching Hospital, Kano
Login to access the Email id

DOI: 10.4103/summ.summ_2_16

Rights and Permissions

Abnormal pulmonary venous connection represents a rare variant of congenital heart disease, in which the pulmonary veins fail to make their normal connection to the left atrium. Instead, they connect and drain anomalously into the systemic venous circulation. The abnormal connection could be partial, when one or more but not all the pulmonary veins connect anomalously or total, when all the pulmonary veins connect anomalously. Total anomalous pulmonary venous connection (TAPVC) is by far the most common and most severe lesion, with a reported prevalence ranging between 1.5% and 2%. Its hemodynamics and clinical features are variable, and diagnosis can be challenging especially in resource-limited setting. This review discusses the embryology and pathogenesis of abnormal pulmonary venous connection, with emphasis on TAPVC. The clinical manifestations and various diagnostic options are also highlighted.

Print this article     Email this article
 Next article
 Previous article
 Table of Contents

 Similar in PUBMED
   Search Pubmed for
   Search in Google Scholar for
 Related articles
 Citation Manager
 Access Statistics
 Reader Comments
 Email Alert *
 Add to My List *
 * Requires registration (Free)

 Article Access Statistics
    PDF Downloaded18    
    Comments [Add]    

Recommend this journal